Truncus arteriosus communis with survival to the age of 46 years: case report.
نویسندگان
چکیده
Truncus arteriosus communis is an uncommon congenital cardiovascular malformation characterized by a single arterial trunk that arises from the base of the heart and gives rise to the coronary, pulmonary and systemic arteries. The prognosis in truncus arteriosus is very poor without surgical correction. The median age at death without surgery ranges from 2 weeks to 3 months, with 85 % mortality by age 1 year. The authors report the autopsy findings of a 46 year old man with truncus arteriosus communis without surgical intervention who died at the hospital shortly after admission.
منابع مشابه
Truncus arteriosus communis. Unusual case associated with transposition.
A child with truncus arteriosus communis, characterized by the posterior origin of an individualized pulmonary trunk is presented. This relationship between the great arteries is unusual in truncus arteriosus communis and the spatial orientation resembles that seen in transposition of the great vessels. A brief discussion is proposed about a proper terminology in this type of complex anomaly.
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1 Collett RW, Edwards JE: Persistent truncus arteriosus: A classification according to anatomic types. Surg Clin N Amer 29: 1245-1270, 1949 2 Tandon R, Hauck AJ, Nadas AS: Persistent truncus arteriosus-A clinical, hemodynamic and autopsy study of nineteen cases. Circulation 28: 1050-1060, 1963 3 Van Praagh R, Van Praagh S: The anatomy of common aortopulmonary trunk ( truncus ateriosus communis ...
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ورودعنوان ژورنال:
- Soudni lekarstvi
دوره 60 3 شماره
صفحات -
تاریخ انتشار 2015